| Gracile ribs are commonly seen in spinal muscular atrophy, congenital myotonic dystrophy and congenital myopathies. |
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| Chronic progressive weakness is the classic presentation in genetic and metabolic myopathies. |
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| Rheumatologists tend to rely on clinical signs, symptoms, and serology, whereas neurologists rely more on histopathology in order to exclude other myopathies. |
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| Neuromuscular diseases are characterized by progressive weakening of skeletal, respiratory, bulbar, and, in the case of myopathies, cardiac muscles. |
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| The idiopathic inflammatory myopathies are relatively rare diseases, and the incidence of dermatomyositis is estimated at 1-10 cases per million in adults. |
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